Congenital anomalous Coronary arteries (CACAs) comprise an important variant of the Coronary vasculature. They are benign in the vast majority of cases, whereas a small minority may be affected by serious consequences such as myocardial infarction, arrhythmia, cardiac arrest, and even death. We herein describe a 62-year-old man with sudden and severe substernal chest pain,Q waves in electrocardiographic leads II, III, and aVF,and positive serum troponin I enzyme. Left heart cardiac catheterization revealed triple Coronary vessel disease with a 60% to 70% occlusion in the left main Coronary artery (LMCA). The left anterior descending (LAD) and the left circumflex artery arose from the ostium of the right Coronary artery. Additionally, a rudimentary type IV dual LAD originated from the LMCA. A Coronary artery bypass graft surgery was performed using a left internal mammary artery graft for the LAD and a saphenous vein graft for the diagonal branches (I & II) of the LAD and the posterior descending artery. The patient was discharged after an uneventful 1-week hospital course.